Calcinosis and lipodystrophy: clinical presentation of 10 years non-treated juvenile dermatomyositis – case report
نویسندگان
چکیده
Methods We describe a 13,5 y old girl presented (april 2011) with extensive calcinosis and lipodystrophy, which were lasting for 10 years, without any treatment. General, musculoskeletal, pulmological and orthodontist evaluations were undertaken. Investigations included multiple radiographs of the calcified regions and chest X-ray, computed-tomography of the lungs, MRI of pelvis, coxofemoral and sacroiliacal joints.
منابع مشابه
Adult onset dermatomyositis associated with lipodystrophy and underlying calcinosis: Case report
Dermatomyositis is an idiopathic inflammatory myopathy, with skin manifestations. A less frequently recognized but clinically important complication of dermatomyositis is lipodystrophy (LD), and associated metabolic abnormalities that increasingly recognized as complications of juvenile dermatomyositis. Lipodystrophy is less frequently reported in adult onset dermatomyositis.In this paper we ar...
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PURPOSE OF REVIEW Over the last few years, there have been several collaborative efforts focusing on how to assess the many aspects of juvenile dermatomyositis (JDM). It has become apparent that skin manifestations are an important part of the disease process that need to be evaluated, treated and controlled. Other extramuscular manifestations, such as calcinosis, are particularly difficult to ...
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Juvenile dermatomyositis (JDM) is considered a multisystemic disease of uncertain etiology. The clinical manifestation is a non-suppurative inflammation of the striated muscle, gastrointestinal tract and skin. Dystrophic calcifications are present in 30%-70% of children with JDM. The clinical case we are presenting is a 4 years old female with diagnosis of JDM in accordance to the Bohan and Pet...
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Juvenile Dermatomyositis (JDM) is a rare autoimmune disease in children and adolescents. In these patients calcinosis might be the most characteristic symptom. However there are only few reported cases of intramuscular calcinosis in Dermatomyositis. We report a case of calcinosis universalis (CU) of the elbow in JDM successfully treated with broaching. The patient, a 24-year-old woman, suffered...
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عنوان ژورنال:
دوره 9 شماره
صفحات -
تاریخ انتشار 2011